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Parry-Romberg Syndrome 환자에서 악정형 및 교정 치료
Orthopedic and Orthodontic Treatments of a Patient with Parry-Romberg Syndrome

대한구순구개열학회지 2012년 15권 1호 p.1 ~ 10

유국호, 백형선,

소속 상세정보

유국호 ( You Kug-Ho ) - 연세대학교 치과대학병원 치과교정학교실
백형선 ( Baik Hyoung-Seon ) - 연세대학교 치과대학병원 치과교정학교실

KMID : 0952820120150010001

Abstract

Parry-Romberg syndrome(PRS) is a degenerative disease characterized by progressive hemifacial atrophy. A 10-year-old girl who had been treated for linear scleroderma at the dermatologic department visited the orthodontic department. The frontal facial photograph showed mild facial asymmetry. On the left side, mild atrophy of soft tissue, enophthalmos, cheek depression, and dry skin with dark pigmentation were observed. The radiograph showed the hypoplasia of both the maxilla and mandible on the left side. This case report describes the treatment of a patient with PRS for 7 years. To minimize the effect of progressive atrophy on the facial growth, a hybrid appliance was used. The facial photos and radiographic records were periodically taken to analyze the progression of PRS. Although it is impossible to prevent the progression of facial asymmetry, it appears to be possible to limit the atrophic effect. After the stabilization of PRS, the orthodontic treatment by the fixed appliance was performed. Additionally, autologous fat graft was performed three times at 6 month intervals. After the treatment, the patient had a confident smile and facial asymmetry was improved.